Noncompaction of ventricular myocardium involving both ventricles.
نویسندگان
چکیده
AIM We aimed to present a case with ventricular myocardial noncompaction involving both ventricles. METHODS AND RESULTS Noncompaction of ventricle is a rare and unclassified congenital cardiac malformation is due to an arrest in intrauterine endomyocardial morphogenesis. We presented a ventricular myocardial noncompaction case involving both left and right ventricles. The physical examination of this case is consistent with mitral regurgitation and the echocardiographic findings are consistent with noncompaction of ventricular myocardium involving both ventricles with left ventricular systolic failure. CONCLUSION Transthoracic echocardiography is a useful clinical tool for diagnosing noncompaction of both the right and left ventricular myocardium. The LVNC definition can also be utilized for RVNC, which this diagnosis has never been reported in a Turkish patient.
منابع مشابه
Biventricular noncompaction: A rare cause of fetal distress and tricuspid regurgitation
Isolated noncompaction of the ventricular myocardium involving both ventricles is a rare entity. Here we report a rare case of biventricular noncompaction presenting with features of fetal distress and moderate tricuspid regurgitation. Noncompaction of both ventricles was diagnosed at birth.
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ورودعنوان ژورنال:
- European journal of echocardiography : the journal of the Working Group on Echocardiography of the European Society of Cardiology
دوره 7 6 شماره
صفحات -
تاریخ انتشار 2006